Description
Periodic and Non-Periodic Fevers, 1st ed. 2020
Rare Diseases of the Immune System Series
Coordinator: Cimaz Rolando
Language: EnglishSubjects for Periodic and Non-Periodic Fevers:
Publication date: 11-2020
283 p. · 15.5x23.5 cm · Paperback
Publication date: 11-2019
283 p. · 15.5x23.5 cm · Hardback
Description
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The book is part of Springer?s series Rare Diseases of the Immune System, which presents recently acquired knowledge on pathogenesis, diagnosis, and therapy with the aim of promoting a more holistic approach to these conditions. Autoinflammatory diseases are hereditary disorders that are caused by single-gene defects in innate immune regulatory pathways and are characterized by a clinical and biological inflammatory syndrome in which there is limited, if any, evidence of autoimmunity. Periodic and Non-Periodic Fevers will be an invaluable source of up-to-date information for all practitioners involved in the care of patients with these disease.
Preface.- I From Pathogenesis to Classification.- 1 Historical notes on Autoinflammatory disorders.- 2 Pathogenesis:Genetic basis, Innate Immunity, Inflammosomes, Cytokines.- 3 Classification and nomenclature of Periodic and Non Periodic fevers.- II Specific diseases.- 4 Mevalonate Kinase Deficiency (MKD).- 5 Tumor necrosis factor receptors associated syndrome (TRAPS).- 6 Cryopyrin-Associated Periodic Syndromes (CAPS).- 7 Pyogenic Arthritis, Pyoderma gangrenosum and Acne Syndrome (PAPA).- 8 Adenosine deaminase syndrome 2 (ADA2).- 9 Interferonopathies.- 10 Inflammatory bone disease.- 11 Amyloidosis.- 12 Dermatologic autoinflammatory diseases.- 13 Autoinflammatory diseases with immunodeficiency.- 14 Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis Syndrome (PFAPA).- 15 Proteasome. related disorders.- 16 Chronic Non-bacterial osteomyelitis.- 17 Systemic JIA and adult onset Still disease.- 18 Behcet disease.- 19 Recurrent idiopathic pericarditis.- 20 Schnitzler syndrome .- Subject Index.
Written by internationally known experts in the field of Periodic and Non-Periodic Fevers
State of the art contents in disease pathogenesis
Wide readership, the book is addressed to specialists in rare disorders
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